Congenital Cardiac Disease Associated with Polysplenia
نویسنده
چکیده
The well-recognized association of congenital cardiac disease with asplenia has been termed "bilateral right-sidedness" or dextro-isomerism, since the spleen is absent, the liver is symmetrical, and each lung has three lobes and an epiarterial bronchus. In a study of pathological material from 12 patients with congenital cardiac disease associated with multiple spleens (as contrasted to accessory spleen), we found a definite tendency for the symmetrical development of organs but with a tendency for bilateral left-sided-
منابع مشابه
Dorsal pancreas agenesis and polysplenia/heterotaxy syndrome: a novel association with aortic coarctation and a review of the literature.
CONTEXT Agenesis of the dorsal pancreas is very rare and may be associated with other congenital disease states. It has a rare association with polysplenia/heterotaxy syndrome. Most commonly, these states occur due to errors in development of the asymmetric organs and may be associated with benign to severe congenital cardiac malformations. CASE REPORT We report a case of a 25-year-old male w...
متن کاملRare congenital anomaly of the inferior vena cava
Congenital anomaly of the inferior vena cava (IVC) is a well described phenomenon [1,2]. These anomalies include complete absence, partial absence or duplication of the IVC [3]. Such anomalies of the IVC are seen more frequently in those with other congenital cardiac anomalies (0.6%–2%) [4]. This congenital condition can be discovered incidentally, or due to symptoms of associated congenital he...
متن کاملHeterotaxia associated with polysplenia.
To cite: Gunes Tatar I, Ergun O, Altunoglu H, et al. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/ bcr-2014-206358 DESCRIPTION A 31-year-old man underwent abdominal CT for blunt abdominal trauma. CT scan demonstrated cardiac apex (figure 1A), stomach (figure 1B, C) and multiple splenic nodules situated on the left of the midsagittal plane; liver and inferior vena c...
متن کاملBiliary Atresia Associated with Polysplenia Syndrome, Dextrocardia, Situs Inversus Totalis and Malrotation of Intestines
Biliary atresia (BA) is a rare disease and the end result of a destructive, inflammatory cholangiopathy, leading to fibrosis and biliary cirrhosis. It is classified into syndromic variety with various congenital anomalies and non-syndromic (isolated anomaly). We present here a 1-month-old female child with the syndromic variety of BA associated with polysplenia syndrome, dextrocardia, situs inv...
متن کاملFrequency of Congenital Heart Disease in Neonates with Extra Cardiac Anomalies
Background Diagnosis of congenital heart disease (CHD) in neonates with extra cardiac anomalies is effective in their clinical management and surgical outcomes. This study aimed to investigate the frequency of CHD in neonates with extra cardiac anomalies admitted to a neonatal intensive care unit (NICU). Material...
متن کامل